ea0022p227 | Clinical case reports and clinical practice | ECE2010
Rodrigues Pedro
, Castedo Jose Luis
, Rocha Madalena
, Guimaraes Patricia
, Guimaraes Jose Eduardo
, Medina Jose Luis
Introduction: POEMS (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes) syndrome is a rare multisystemic disease. Diagnosis requires two major criteria and at least one minor criterion. Major criteria include polineuropathy and a monoclonal plasma proliferative disorder (almost always lambda). Minor criteria include osteosclerotic bone lesions, Castleman disease, organomegaly (including lymphadenopathy), oedema, pleural effusion or ascites, e...